Dyke-Davidoff-Masson Syndrome- A Rare Cause of Refractory Epilepsy
Prerna Malik
Department of Psychiatry, Pt. BDS University of Health Sciences, Rohtak, Haryana, India
Anil kumar D. Gulia *
Department of Orthopaedics, BPS Government Medical College, Khanpur Kalan, Sonepat, Haryana, India
Rajinder Garg
Gian Sagar Medical College and Hospital, Banur, Punjab, India
Preeti Singh
Department of Psychiatry, Pt. BDS University of Health Sciences, Rohtak, Haryana, India
*Author to whom correspondence should be addressed.
Abstract
DDMS is a rare syndrome characterized by seizures, facial asymmetry, contralateral hemiplegia and mental retardation. The characteristic radiologic features are cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. Dyke-Davidoff-Masson Syndrome (DDMS) is one among the syndromes associated with refractory epilepsy. We report a case of DDMS in an 18 year old female who presented with seizures, hemiparesis of the right side and mental retardation. Computed tomography on this patient assisted in making a diagnosis of DDMS.
Keywords: Dyke Davidoff Masson syndrome, refractory epilepsy, cerebral hemiatrophy